Tuberous Sclerosis Complex Research

Wunderlich syndrome (WS) is a rare, potentially life-threatening spontaneous renal or perirenal hemorrhage, usually caused by renal neoplasms or vascular disorders. Hemodialysis patients are at higher risk due to uremic platelet dysfunction, dialysis-related hemostatic abnormalities, and acquired cystic kidney disease…

Wunderlich syndrome (WS) is a rare, potentially life-threatening spontaneous renal or perirenal hemorrhage, usually caused by renal neoplasms or vascular disorders. Hemodialysis patients are at higher risk due to uremic platelet dysfunction, dialysis-related hemostatic abnormalities, and acquired cystic kidney disease…

Objective: The clinicopathological characteristics and survival outcomes of rare primary renal tumor cases treated surgically were evaluated and compared with the literature. Material and Methods: A total of 517 patients who underwent partial or radical nephrectomy for renal mass between January 2020-January 2025 were…

Subependymal giant cell astrocytoma (SEGA) usually arises near the foramen of Monro in patients with tuberous sclerosis complex (TSC). A 14-year-old boy presented with headache and a 6.2 × 5.8 cm extraventricular, cyst-dominant hemispheric lesion containing a mildly enhancing mural nodule. Microsurgical excision was p…

Introduction. Wilms tumor is the most common renal malignancy in children. Survival rates now exceed 90% with multimodal therapy. This study aims to retrospectively analyze 104 pediatric Wilms tumor patients diagnosed over a 47-year period at our institution, examining demographic characteristics, tumor staging, treat…

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Hamartomas are well-recognized benign growths associated with tuberous sclerosis complex (TSC), occurring frequently in the skin, central nervous system, and kidneys. Although musculoskeletal manifestations have been documented, intra-articular hamartomas originating specifically from the joint capsule have not been p…

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Aim: The study aims to evaluate the efficacy and safety of selective arterial embolization (SAE) for renal angiomyolipoma (rAML).Material and Methods: This retrospective study included patients with rAML who underwent SAE between February 2009 and December 2022. The primary outcome was procedural success, defined as c…