Pars Plana Vitrectomy with Foveal Cyst Aspiration as a Treatment Option for Macular Retinoschisis in a Coat-Like Retinitis Pigmentosa Case

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PURPOSE: To present a patient with macular retinoschisis in coat-like retinitis pigmentosa (RP) who underwent pars plana vitrectomy with foveal cyst aspiration. METHODS: Case report involving clinical examination, fundus photography, fluorescein angiography, optical coherence tomography, B-scan ultrasonography, and surgical video. RESULTS: A 45-year-old female with CRB1 mutation related RP was referred for vitreoretinal surgery due to macular detachment. The patient was diagnosed with bilateral bullous macular retinoschisis secondary to Coats-like RP. The patient received a total of six anti-VEGF injections and laser ablation of telangiectatic vessels twice in both eyes without any response. Both eyes underwent pars plana vitrectomy, cyst aspiration with 39G needle, endolaser to telangiectatic vessels, and sulfur hexafluoride tamponade one month apart. The surgical treatment resulted in anatomical and functional improvement. CONCLUSION: Surgical microaspiration of macular cyst may be an option for patients with severe cystic macular retinoschisis in Coats-like RP.